Volume 1 – Tabular list - Tabular list of inclusions and four-character subcategories - III: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

D65 Disseminated intravascular coagulation [defibrination syndrome]

Incl.:

Afibrinogenaemia, acquired

Consumption coagulopathy

Diffuse or disseminated intravascular coagulation [DIC]

Fibrinolytic haemorrhage, acquired

Purpura:

• fibrinolytic
• fulminans

Excl.:

that (complicating):

• abortion or ectopic or molar pregnancy (O00-O07, O08.1)
• in newborn (P60)
• pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

D66 Hereditary factor VIII deficiency

Incl.:

Deficiency factor VIII (with functional defect)

Haemophilia:

• NOS
• A
• classical

Excl.:

factor VIII deficiency with vascular defect ( D68.0)

D67 Hereditary factor IX deficiency

Incl.:

Christmas disease

Deficiency:

• factor IX (with functional defect)
• plasma thromboplastin component [PTC]

Haemophilia B

D68 Other coagulation defects

Excl.:

those complicating:

• abortion or ectopic or molar pregnancy (O00-O07, O08.1)
• pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

D68.0 Von Willebrand disease

Incl.:

Angiohaemophilia

Factor VIII deficiency with vascular defect

Vascular haemophilia

Excl.:

capillary fragility (hereditary) ( D69.8)

factor VIII deficiency:

• NOS (D66)
• with functional defect (D66)

D68.1 Hereditary factor XI deficiency

Incl.:

Haemophilia C

Plasma thromboplastin antecedent [PTA] deficiency

D68.2 Hereditary deficiency of other clotting factors

Incl.:

Congenital afibrinogenaemia

Deficiency:

• AC globulin
• proaccelerin

Deficiency of factor:

• I [fibrinogen]
• II [prothrombin]
• V [labile]
• VII [stable]
• X [Stuart-Prower]
• XII [Hageman]
• XIII [fibrin-stabilizing]

Dysfibrinogenaemia (congenital)

Hypoproconvertinaemia

Owren disease

D68.3 Haemorrhagic disorder due to circulating anticoagulants

Incl.:

Haemorrhage during long-term use of anticoagulants

Hyperheparinaemia

Increase in:

• antithrombin
• anti-VIIIa
• anti-IXa
• anti-Xa
• anti-XIa

Coding-Hint

Use additional external cause code (Chapter XX), if desired, to identify any administered anticoagulant.

Excl.:

long-term use of anticoagulants without haemorrhage ( Z92.1)

D68.4 Acquired coagulation factor deficiency

Incl.:

Deficiency of coagulation factor due to:

• liver disease
• vitamin K deficiency

Excl.:

vitamin K deficiency of newborn ( P53)

D68.5 Primary thrombophilia

Incl.:

Activated protein C resistance [factor V Leiden mutation]

Deficiency:

• antithrombin
• protein C
• protein S

Prothrombin gene mutation

D68.6 Other thrombophilia

Incl.:

Anticardiolipin syndrome

Antiphospholipid syndrome

Presence of the lupus anticoagulant

Excl.:

disseminated intravascular coagulation ( D65)

hyperhomocysteinemia ( E72.1)

D69 Purpura and other haemorrhagic conditions

Excl.:

benign hypergammaglobulinaemic purpura ( D89.0)

cryoglobulinaemic purpura ( D89.1)

essential (haemorrhagic) thrombocythaemia ( D47.3)

purpura fulminans ( D65)

thrombotic thrombocytopenic purpura ( M31.1)

D69.0 Allergic purpura

Incl.:

Purpura:

• anaphylactoid
• Henoch(-Schönlein)
• nonthrombocytopenic:
  • —  haemorrhagic
  • —  idiopathic
• vascular

Vasculitis, allergic

D69.1 Qualitative platelet defects

Incl.:

Bernard-Soulier [giant platelet] syndrome

Glanzmann disease

Grey platelet syndrome

Thromboasthenia (haemorrhagic)(hereditary)

Thrombocytopathy

Excl.:

von Willebrand disease ( D68.0)

D69.2 Other nonthrombocytopenic purpura

Incl.:

Purpura:

• NOS
• senile
• simplex

D69.3 Idiopathic thrombocytopenic purpura

Incl.:

Evans syndrome

D69.4 Other primary thrombocytopenia

Excl.:

thrombocytopenia with absent radius ( Q87.2)

transient neonatal thrombocytopenia ( P61.0)

Wiskott-Aldrich syndrome ( D82.0)

D69.5 Secondary thrombocytopenia

Coding-Hint

Use additional external cause code (Chapter XX), if desired, to identify cause.

D69.8 Other specified haemorrhagic conditions

Incl.:

Capillary fragility (hereditary)

Vascular pseudohaemophilia